Case Report
A Case of Thrombotic Thrombocytopenia Purpura Associated with Systemic Lupus Erythematosus: Diagnostic Utility of ADAMTS-13 Activity
Table 1
Laboratory test results on admission.
| Blood test | | | | WBC | 5100/mm3 | CH50 | 21 U/mL | Neutro | 45.5% | C3 | 81 mg/dL | Lymph | 45.5% | C4 | 8 mg/dL | Mono | 6.0% | IgG | 1525 mg/dL | Eo | 0% | IgA | 190 mg/dL | Baso | 0% | IgM | 40 mg/dL | RBC | 219/mm3 | ANA | ×320 | Reticuro | 7.2% |
Speckled |
×320 | Hb | 6.4 g/dL | Anti-DNA antibody (RIA) | 27 IU/mL | Hct | 18.0% | Anti-SS-A antibody | 1160 U/mL | Plt | 0.4/mm3 | Anti-SS-B antibody | (−) | PT-INR | 1.11 | Anti-Topo-1 antibody | (−) | ATPP | 29.1 sec (contro; 30.3 sec) | Anti-RNP antibody | 184 U/mL | FDP | 17.4 μg/dL | Anti-Sm antibody | (−) | D-D | 8.78 μg/dL | MPO-ANCA | (−) | ESR | 66 mm/h | Anti cardiolipin antibody (IgG) | 13 U/mL | TP | 6.9 g/dL | Anti-CLβ2GP1 antibody | (−) | ALB | 3.7 g/dL | LAC | (−) | BUN | 10 mg/dL | Anti platlet antibody | (−) | Cr | 0.54 mg/dL | PA-IgG | 2150 ng/107 cell | UA | 3.0 mg/dL | IC-C1q | 3.3 μg/mL | Na | 136 mmol/L | Direct Coombs test | (−) | K | 3.9 mmol/L | Indirect Coobms test | (−) | CL | 102 mmol/L | CMV IgG | (+) | T-Bil | 2.9 mg/dL | CMV IgM | (−) | D-Bil | 0.9 mg/dL | CMV Ag | (−) | AST | 61 IU/L | EBV EBNA | (−) | ALT | 35 IU/L | EBV-VCAIgG | (+) | LDH | 915 IU/L | EBV Ag | (+) | CK | 77 IU/L | EBV-VCAIgM | (−) | CRP | <0.3 mg/dL | HBs Ag | (−) |
| Urianalysis | | | | Glu | (−) | | | Protein | (−) | | | RBC | (−) | | | WBC | (−) | | | abnormal cyst | (−) | | |
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