Case Report

A Case of Thrombotic Thrombocytopenia Purpura Associated with Systemic Lupus Erythematosus: Diagnostic Utility of ADAMTS-13 Activity

Table 1

Laboratory test results on admission.

Blood test
WBC5100/mm3CH5021 U/mL
 Neutro45.5%C381 mg/dL
 Lymph45.5%C48 mg/dL
 Mono6.0%IgG1525 mg/dL
 Eo0%IgA190 mg/dL
 Baso0%IgM40 mg/dL
RBC219/mm3ANA×320
Reticuro7.2% Speckled ×320
Hb6.4 g/dLAnti-DNA antibody (RIA)27 IU/mL
Hct18.0%Anti-SS-A antibody1160 U/mL
Plt0.4/mm3Anti-SS-B antibody(−)
PT-INR1.11Anti-Topo-1 antibody(−)
ATPP29.1 sec (contro; 30.3 sec)Anti-RNP antibody184 U/mL
FDP17.4 μg/dLAnti-Sm antibody  (−)
D-D8.78 μg/dLMPO-ANCA(−)
ESR66 mm/hAnti cardiolipin antibody (IgG)13 U/mL
TP6.9 g/dLAnti-CLβ2GP1 antibody(−)
ALB3.7 g/dLLAC(−)
BUN10 mg/dLAnti platlet antibody(−)
Cr0.54 mg/dLPA-IgG2150 ng/107 cell
UA3.0 mg/dLIC-C1q3.3 μg/mL
Na136 mmol/LDirect Coombs test(−)
K3.9 mmol/LIndirect Coobms test(−)
CL102 mmol/LCMV IgG(+)
T-Bil2.9 mg/dLCMV IgM(−)
D-Bil0.9 mg/dLCMV Ag(−)
AST61 IU/LEBV EBNA(−)
ALT35 IU/LEBV-VCAIgG(+)
LDH915 IU/LEBV Ag(+)
CK77 IU/LEBV-VCAIgM(−)
CRP<0.3 mg/dLHBs Ag(−)

Urianalysis
Glu(−)
Protein(−)
RBC(−)
WBC(−)
abnormal cyst(−)