Clinical Study
Illness Severity, Social and Cognitive Ability, and EEG Analysis of Ten Patients with Rett Syndrome Treated with Mecasermin (Recombinant Human IGF-1)
Table 2
Positive and negative features of the novel Rett Severity Score (RSS).
| Rett Severity Score features | Positive features | Negative features |
| Pointing | Hand wringing | Manipulating | Biting | Reaching for something | Rocking | Ability to mimic/imitate | Hitting | Indicating yes/no with head gesture | Indiscriminate moaning | Reactivity to a call | Tongue, chewing | Reactivity to an object | Vacant staring |
Siming to stimulus | Bruxism | Deliberate Vocalisation | Breath holding, apnoea | Attention | Valsalva Maneuver |
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A full description can be found in the supplementary materials of the present paper.
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