Nosology of Juvenile Muscular Atrophy of Distal Upper Extremity: From Monomelic Amyotrophy to Hirayama Disease—Indian Perspective

<table>Wasting of  hands and forearms with oblique amyotrophy (black arrows) (a); electromyography showing normal motor unit action potential in right deltoid (b); neurogenic motor unit action potential in right abductor pollicis brevis (c); incomplete interference pattern on submaximal volition in right abductor pollicis brevis (d). </table>

BioMed Research International

fig1

Figure 1

Figure 1: Nosology of Juvenile Muscular Atrophy of Distal Upper Extremity: From Monomelic Amyotrophy to Hirayama Disease—Indian Perspective 