Review Article

Nosology of Juvenile Muscular Atrophy of Distal Upper Extremity: From Monomelic Amyotrophy to Hirayama Disease—Indian Perspective

Figure 4

Two young males (a) and (b) with proximal left upper limb weakness and wasting without the typical findings described in Figures 1 to 3: marked wasting proximal left upper limbs (black arrow) (A) and mild/no wasting distal left upper limbs in same patients (B), preserved or mild loss of cervical lordosis and absence of localized cord atrophy at corresponding C5, 6 segments (C), normal cervical cord outline without loss of attachment of dura from subjacent lamina at all levels on neutral position axial T2WI MRI (D), and no posterior epidural crescentic enhancing mass on flexion contrast sagittal T1WI MRI (E).
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(a)
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(b)