Clinical Study

Pulmonary Hypertension in Portugal: First Data from a Nationwide Registry

Table 1

Demographic, clinical, and hemodynamic characteristics of pulmonary arterial hypertension (PAH) and chronic thromboembolic pulmonary hypertension (CTEPH) incident patients at baseline.

Total ( )PAH ( )CTEPH ( ) value

Age (years)50.5 ± 17.043.4 ± 16.460.3 ± 12.5<0.001
Female gender, (%)53 (67.1%)30 (65.2%)23 (69.7%)0.676
Six-minute test walking distance (m)351.3 ± 137.4370.8 ± 140.1320.4 ± 132.90.327
Functional class, (%)
 I1 (1%)1 (2%)0 (0%)0.565
 II17 (25%)11 (27%)6 (21%)
 III34 (49%)21 (51%)13 (46%)
 IV17 (25%)8 (20%)9 (32%)

Hemodynamic data

Right atrial pressure (mmHg)9.1 ± 5.87.7 ± 5.911.0 ± 5.20.015
Mean pulmonary artery pressure (mmHg)49.1 ± 15.150.6 ± 17.947.1 ± 9.90.313
Cardiac output (L·min−1)4.4 ± 1.94.5 ± 1.84.3 ± 20.778
Cardiac index (L·min−1·m−2)2.6 ± 1.12.7 ± 1.12.5 ± 1.10.406
Pulmonary capillary wedge pressure (mmHg)9.7 ± 3.39.5 ± 3.59.9 ± 3.10.587
Pulmonary vascular resistance (Wood units)11.1 ± 6.411.4 ± 6.510.8 ± 6.30.729