Exploring Clinical and Epidemiological Characteristics of Interstitial Lung Diseases: Rationale, Aims, and Design of a Nationwide Prospective Registry—The EXCITING-ILD Registry

Table 2

ILD patients and subtypes eligible for enrolment in the EXCITING-ILD registry.

Idiopathic interstitial pneumonias (IIPs)	Idiopathic pulmonary fibrosis (IPF); Idiopathic nonspecific interstitial pneumonia (NSIP); Desquamative interstitial pneumonia (DIP); Respiratory bronchiolitis-associated interstitial lung disease (RB-ILD); Cryptogenic organising pneumonia (COP); Idiopathic lymphoid interstitial pneumonia (LIP); Acute interstitial pneumonia (AIP); Rare forms of IIPs (e.g., pleuropulmonary fibroelastosis); Nonclassifiable IIP
Granulomatous lung disease	Sarcoidosis; Berylliosis; Other (e.g., involvement in chronic inflammatory liver and gut diseases, except EAA)
Hypersensitivity pneumonitis (extrinsic allergic alveolitis (EAA))	Farmer’s lung; Bird keepers’ lung disease; Origin unknown; Other
Rheumatic and connective tissue diseases with pulmonary involvement such as	Connective tissue disease (subtype); Vasculitis; Rheumatoid arthritis
Pneumoconiosis	Asbestosis; Silicosis; Other
Other forms	Pulmonary lymphangioleiomyomatosis; Pulmonary Langerhans’ cell histiocytosis; Pulmonary alveolar proteinosis; Eosinophilic pneumonia; Post-ARDS fibrosis
Drug-related
Radiotherapy associated
Fibrosis in emphysema patients without signs of other ILDs (CPFE)
Others
Not classifiable

For each subtype it will be queried whether or not a diagnosis of concomitant emphysema in ILD was made.