| | Authors | Year | | M (F) | Age at Dx | Race | Location of tumor | Treatment | Surgical method | Mean f/u period (months) | 5-year OSR (%) | 5-year DFSR (%) | 2-year OSR (%) | 2-year DFSR (%) | MS (months) |
| 1 | Hodgkinson et al. [12] | 1979 | 13 | 7 (6) | 66 (51–80) | NR | Head and neck | S (5), S + RT (5), RT (3) | NR | 13 (1–96) | NR | NR | NR | NR | NR |
| 2 | Holden et al. [4] | 1987 | 72 | 44 (28) | 74 (56–92) | C | Scalp and face | S + RT (3), RT (69) | NR | NR (12–144) | 12 | NR | 29 | NR | 15 |
| 3 | Mark et al. [7] |
1996 | 28 | 21 (7) | 61 (6–83) | NR | Head and neck | S (12), S + CT (3), S + RT ± CT (6), RT ± CT (7) | NR | 32 (3–159) | NR | 26 | NR | NR | NR |
| 4 | Lydiatt et al. [6] | 1994 | 18 | 13 (5) | 67 | C (17) | Head and neck | S (6), S + RT (2), S + CT (1), CT (9) | NR | NR | 33 | 20 | NR | NR | NR |
| 5 |
Morrison et al. [19] | 1995 | 14 | 8 (6) | 66 (49–83) | C | Scalp and face | S + RT (6), RT (3), S ± RT ± CT (11) | STSG | NR | 29 | NR | NR | NR | 22 |
| 6 | Pawlik et al. [11] | 2003 | 29 | 18 (11) | 71 (33–90) | C (28), A (1) | Scalp | S + RT (28), RT (1) | WE, LF (2), and STSG (26) | 18.3 (3.2–106) | 12 | NR | NR | NR | 28.4 |
| 7 | Ohguri et al. [20] | 2005 | 20 | 11 (9) | 71 (49–91) | A (J) | Scalp | RT + IT | NR | 29.5 (5–120) | NR | NR | NR | NR | 36.2 |
| 8 | Buschmann et al. [16] | 2008 | 19 | 14 (5) | 77 (59–86) | NR | Scalp | S ± RT ± CT | Oc + STSG | NR | NR | NR | NR | NR | 17.2 |
| 9 |
Köhler et al. [21] | 2008 | 23 | 11 (12) | 63 (12–75) | C (19), AA (3), and A (1) | Head and neck | S + RT (19), S + CT (2), S + RT + CT (2) | WE (2 cm) | 19.7 (5–108) | 21.7 | NR | NR | NR | NR |
| 10 | Lim et al. [22] | 2010 | 9 | 5 (4) | 71 (64–82) | A (K) | Scalp | S ± RT (8) | WE (5 cm) + Oc + LD + STSG + Pr + Nd | 24 | NR | NR | NR | 100 | 15 |
| 11 |
Ogawa et al. [23] | 2012 | 48 | 29 (19) | 77 (58–94) | A (J) | Scalp and face | S + RT ± CT ± IT (17), S + CT + IT (2), RT ± CT ± IT (20), RT (5), and IT (4) | WE (3–5 cm) | 13.7 (2.5–105.9) | NR | NR | 22.1 | NR | 13.4 |
| 12 |
Dettenborn et al. [24] | 2014 | 80 | 50 (30) | 71 (SD 14.4) | NR | Head and neck | S (32), S + RT (38), S + CT (4), and S + RT + CT (6) | NR | 55.3 (SD 74.4) | 54 | NR | 71 | NR | 64.0 (CI 48.4–75.6) |
| 13 |
Mullins and Hackman [5] | 2015 | 6 | 5 (1) | 66 (52–83) | C (4), AA (2) | Head and neck | S (1), S + RT (2), S + RT + CT (1), and C (2) | NR | 42 | NR | NR | NR | 20 | 36.7 (5–76) |
| 14 | Patel et al. [14] | 2015 | 55 | 39 (16) | NR | NR | Scalp and face | S ± RT ± CT (39) | NR | 25.2 (4.7–227.1) | 38 | 16 | NR | NR | 25.2 |
| 15 | Our study | 2015 | 14 | 13 (1) | 69 (52–81) | A (K) | Scalp | S (3), S + RT (3), S + CT (3), and S + RT + CT (5) | WE (1–5 cm) | 17 (8–87) | 15 | 7.7 | 75 | 38.7 | 31 (CI 27.0–37.0) |
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