Treatment and Patient Reported Outcome in Children with Hirschsprung Disease and Concomitant Congenital Heart Disease

Table 1

The different types of congenital heart diseases (CHD) identified among 13 out of 53 children with Hirschsprung disease (HD). PFO = patent foramen oval, ASD = atrial septal defect, and VSD = ventricular septal defect.

HD and CHD	Congenital heart disease
Patient 1	PFO or small ASD, with left to right shunt without restrictions
Patient 2	PFO with left to right shunt
Patient 3	Perimembranous ventricular septal defect (VSD) and ASD 4-5 mm
Patient 4	Muscular VSD, 3 mm
Patient 5	Dysplastic tricuspid valve with moderate insufficiency, pulmonic insufficiency, ductus with bidirectional flow
Patient 6	Small PFO and small ductus shunt;
Patient 7	Small central ASD and atrial septal aneurysm
Patient 8	Bicuspid aortic valve
Patient 9	Aortic stenosis, dysplastic aortic valve stenosis
Patient 10	ASD 3-4 mm, minimal ductus;
Patient 11	ASD without hemodynamic effect
Patient 12	Open PFO 4 mm, open ductus, left periphery pulmonary artery stenosis
Patient 13	ASD, obvious left to right shunt, 7 mm. Enlargement of both atriums and mild branch artery stenosis in arteria pulmonalis

Defined as mild forms of CHD.
Excluded in long-term follow-up because they were <4 years old.