Clinical and Instrumental Characteristics of Newly Diagnosed Patients with Various Forms of Pulmonary Hypertension according to the Russian National Registry
Table 4
Examination data for patients with PAH and CTEPH at the time of diagnosis.
Signs
Patient groups
PAH
IPAH
PAH-CTD
PAH-CHD
PoPH
CTEPH
Lips cyanosis, acrocyanosis
192 (39.4%)4
62 (31.5%)2.5
23 (24.5%)3
109 (61.2%)4.5
1 (11.1%)
46 (22.3%)
Сlubbed fingers/watch-glass nails
47 (9.7%)4
3 (1.5%)2
0 (0%)3
59 (33.1%)4.5
0 (0%)
1 (0.5%)
Accentuated P2
471 (96.7%)
197 (98.9%)5
92 (97.9%)5
177 (99.4%)5
6 (66.7%)
192 (93.2%)5
Systolic murmur localized at left sternal border
431 (88.5%)
185 (92.9%)1.5
70 (74.5%)3
163 (91.5%)5
5 (55.5%)
168 (81.5%)5
Pulmonary insufficiency
112 (22.9%)
45 (22.6%)1.5
10 (10.6%)3.4.5
48 (26.9%)5
0 (0%)
41 (19.9%)5
Wheezing
18 (3.7%)4
10 (5.1%)2.4.5
5 (5.3%)3.4.5
1 (0.6%)4
0 (0%)
56 (27.2%)5
Varicose veins
8 (1.6%)4
2 (1.0%)
1 (1.1%)
5 (2.8%)
0 (0%)
18 (8.7%)5
Swelling of the legs/feet
106 (27.8%)4
71 (35.7%)1.2.4.5
18 (19.1%)4.5
43 (24.2%)4.5
0 (0%)
142 (68.9%)5
Hepatomegaly
38 (7.8%)4
20 (10.1%)2.5
6 (6.4%)
3 (1.8%)5
6 (66.7%)
62 (30.1%)5
Ascites
9 (1.8%)
8 (4.0%)1.2.4
0 (0%)4
0 (0%)4
0 (0%)
10 (4.8%)5
Note: 1: ; 2: ; 3: ; 4: vs. the CTEPH ; 5: vs. the group of .
