Research Article
Time to Start Delivering Iron Chelation Therapy in Newly Diagnosed Severe β-Thalassemia
Table 1
The characteristic of subjects at diagnosis and at SF level >1000 ng/mL.
| Characteristic | At diagnosis () | At SF level >1000 ng/mL () |
| Iron status | SF (ng/mL); ; median (IQR) | ; 319.5 (65.2–768.3) | ; 1,175.5 (1,002–1,508) | TS (%); ; median (IQR) | ; 70.0 (20.1–98.7) | ; 82.6 (30.1–100.0) | Hepcidin level (ng/mL); ; median (IQR) | ; 255.0 (114.5–363.5) | ; 366.6 (176.1–876.0) | Serum iron (μg/dL); ; median (IQR) | ; 173 (45–330) | ; 189 (71–261) | TIBC (μg/dL); ; median (IQR) | ; 265 (132–367) | ; 230 (153–345) | Amount of transfusion when SF level >1000 ng/mL; ; median (IQR) | ; 8 (4–12) | Type of thalassemia; (%) | β-Thalassemia mayor | 38 (90) | Severe HbE/β-thalassemia | 4 (10) | Age (month); ; median (IQR) | ; 7.5(2–24) | Gender; (%) | Male | 22 (52) | Female | 20 (48) | Hb (g/dL); ; median (IQR) | ; 5.2 (1.6–7.8) | Dietary status; (%) | Exclusive breastfeeding | Yes | 42 (100%) | No | 0 (0%) | Continued breastfeeding until 2 years old | Yes | 30 (71.4%) | No | 12 (38.6%) | Complementary foods | Yes | 42 (100%) | No | 0 (0%) |
|
|