| | Paper | Age (years), sex | ANCA | Miscellaneous features |
| | Bonaci-Nikolic et al., 2010 [6] | 63, F | MPO | — | | 51, F | MPO | — | | 24, F | MPO | — |
| | Cojocaru et al., 2007 [42] | Mean 75 | 21 PR3 | Concomitant ischemic stroke |
| | Cojocaru et al., 2006 [43] | ? | ? | — |
| | Gatselis et al., 2006 [44] | ? | 65 c-ANCA, 4 p-ANCA (though all negative for PR3 and MPO) | |
| | Lamprecht et al., 2003 [9] | ? | 6 bactericidal/permeability-increasing proteins | Mixed cryoglobulinemia | | 4 cathepsin G proteins | | 1 unknown antigen (c-ANCA) | | 2 bactericidal/permeability-increasing proteins | No cryoglobulinemia | | Four patients: cathepsin G |
| | Zandman-Goddard et al., 2003 [45] | 34, M | c-ANCA and p-ANCA | Complicated by transverse myelitis |
| |
Tajima et al., 2002 [46] | 66, F | p-ANCA | Complicated by pachymeningitis |
| | Wu et al., 2002 [47] | ? | 253 PR3,
25 PR3 and MPO | Higher proportion of ANCA-positive compared to ANCA-negative patients with high alanine aminotransferase, high alpha-fetoprotein, skin disease, cirrhosis, and anemia |
| | Agarwal et al., 2001 [48] | ? | 5 p-ANCA | — |
| | Igaki et al., 2000 [49] | 60, F | MPO | Glomerulonephritis, cryoglobulinemia |
| | Lamprecht et al., 1998 [50] | 60, F | c-ANCA | Type II cryoglobulinemia |
| | Ohira et al., 1998 [51] | ? | 12 c-ANCA or p-ANCA | — |
| | Kallinowski et al., 1997 [52] | ? | 5 ANCA | — |
| | Papi et al., 1997 [53] | 63, F | MPO | Mixed type II cryoglobulinemia, leukocytoclastic vasculitis on skin biopsy |
| |
Dalekos and Tsianos, 1994 [54] | ? | 3 ANCA | — |
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