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Case Reports in Anesthesiology
Volume 2016, Article ID 4659891, 3 pages
Case Report

An Unexpected Airway Complication in a Male Patient with Goltz Syndrome

1Penn State Milton S. Hershey Medical Center, 500 University Drive, H187, Hershey, PA 17033, USA
2Penn State Hershey Anesthesia, 500 University Drive, H187, Hershey, PA 17033, USA

Received 29 June 2016; Accepted 21 August 2016

Academic Editor: Richard Riley

Copyright © 2016 Sadie Smith et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


Goltz syndrome, also known as focal dermal hypoplasia, is a rare X-linked dominant multisystem syndrome presenting with cutaneous, skeletal, dental ocular, central nervous system and soft tissue abnormalities. This case report discusses an adult male patient with Goltz syndrome that was noted to have large, papillomatous, hypopharyngeal lesions upon induction of general anesthesia. We highlight challenges with airway management intraoperatively and postoperatively in patients with Goltz syndrome. Our aim is to increase awareness of the potential airway complications associated with this genetic disorder and to provide suggestions for optimal perioperative management for patients afflicted with Goltz syndrome.