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Case Reports in Anesthesiology
Volume 2018 (2018), Article ID 7862327, 4 pages
Case Report

Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery

1Department of Anesthesiology and Critical Care Medicine, MediClin Heart Institute Lahr/Baden, Lahr, Germany
2Department of Cardiac Surgery, MediClin Heart Institute Lahr/Baden, Lahr, Germany

Correspondence should be addressed to J. N. Hilberath

Received 16 November 2017; Accepted 16 January 2018; Published 13 February 2018

Academic Editor: Anjan Trikha

Copyright © 2018 S. Viehmeyer et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


Freeman-Sheldon syndrome (FSS) or “whistling face” syndrome is a rare congenital disorder complicated by characteristic facial deformities and muscular contractures. We report on a 64-year-old male patient presenting for surgical replacement of his aortic valve and review the available literature on anesthetic considerations and perioperative management principles. FSS frequently poses a significant challenge to airway management and gaining vascular access. Moreover, these patients are reportedly at risk for developing malignant hyperthermia (MH) or neuroleptic malignant syndrome.