Case Report

Myotonic Dystrophy and Anesthetic Challenges: A Case Report and Review

Table 1

Review of reported cases of anesthesia in patients with myotonic dystrophy over last ten years.

AuthorType of AnesthesiaType of SurgeryComplications

Gorelick L. et al. 2018
Case series (3 cases) [5]
MAC sedation and
general
EP study and pacemaker insertionOne patient develops arrhythmias/atrial fibrillation during the procedure

Uno et al. 2017 [6]General with propofol infusion, rocuronium, and sugammadex for reversal.
TAP block and epidural for pain
Laparoscopic cholecystectomynone

Subramaniam et al. 2016 [7]General and epiduralOpen resection of pheochromocytoma/paragangliomanone

Gaszynski T. 2016 [8]General with propofol and dexmedetomidine infusionslaparoscopic
cholecystectomy
none

Corriea M. et al. 2016 [9]Continuous spinalLaparoscopic cholecystectomynone

Gurunathan U. et al. 2015 [8]General with propofol/remifentanil infusion and reversal with sugammadexLaparoscopic cholecystectomynone

Urciuoli P. et al. 2014
Case series (2 cases) [10]
General and thoracic epidural anesthesia without muscle relaxantLaparoscopic cholecystectomynone

Piccard A. et al. 2013[11]General and sugammadex. use of acceleromyographyPEG insertion, orchiopexy, and tongue tie releasecongenital MD

Stourac P. et al. 2013 [12]
Case series(2 cases)
General with sugammadex reversalCesarean section x 2 in same patientremain intubated in ICU for 2 hours first time

Bissinoto FM et al.[13]General with propofol and remifentanil infusion and reversal with prostigmineLaparoscopic cholecystectomyPatient developed myotonia after extubation, unable to intubate, maintained ventilation with LMA for few hours.