Successful Treatment of an Infant with Left Ventricular Noncompaction Presenting with Fatal Ventricular Arrhythmia Treated with Cardiac Resynchronization Therapy and an Implantable Cardioverter Defibrillator

Figure 1

Electrocardiogram (ECG) and arterial blood pressure monitoring on admission (a). (Top panel) ECG shows polymorphic ventricular tachycardia, with a rate of approximately 300 bpm. (Bottom panel) arterial blood pressure monitoring. (b) Lead II of the ECG after polymorphic ventricular tachycardia was stopped. The heart rate (HR) was 79 bpm, PR interval was 160 msec, and QTc interval was 510 msec with alternate T waves. (c) Chest X-ray on admission showing a cardiothoracic ratio of 52%. Transthoracic echocardiography on admission. (d) Transthoracic echocardiography shows left ventricular noncompaction on the parasternal short axis view, with a ratio of noncompacted to compacted area at end-systole > 2. (e) Color Doppler imaging reveals communication between myocardial recesses and the left ventricular cavity. (f) The 12-lead ECG before implantable cardioverter defibrillator (ICD) implantation, showing 2 : 1 atrioventricular block. The HR was 76 bpm, PR interval was 170 msec, and QTc interval was 462 msec. P indicates the P wave in lead II.

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