Case Report

Successful Use of Pulmonary Vasodilators in Acute Chest Syndrome Complicated by Persistent Right Ventricular Failure

Table 1

Hemodynamics on right heart catheterization nineteen months prior to hospitalization (baseline) in comparison to during acute chest syndrome (ACS).

BaselineACS

Mean right atrial pressure5 mmHg18 mmHg
Right ventricular pressure40/3 mmHg89/10 mmHg
Pulmonary artery pressure (mean)42/16 (25) mmHg95/46 (58) mmHg
Pulmonary capillary wedge pressure6 mmHg10 mmHg
Pulmonary vascular resistance3.9 Wood units13.6 Wood units
Cardiac output by thermodilution4.83 L/min3.53 L/min
Cardiac index by thermodilution2.57 L/min/m21.86 L/min/m2
Arterial oxygen saturation97%98%
Pulmonary artery oxygen saturation69%53%
Hemoglobin12.4 g/dL10.6 g/dL