Case Report

Oral and Dental Findings of Dyskeratosis Congenita

Table 2

Oral and dental findings in dyskeratosis congenita.

FindingsLiteratures

Dental findings
 HypodontiaBrown [2], Baran et al. [4], and Atkinson et al. [5].
 Short blunted rootsAbdel-Karim et al. [1], Brown [2], Atkinson et al. [5], Hölttä et al. [8], and Thomas [17].
 Extensive caries lesionsAbdel-Karim et al. [1], Davidovich et al. [3], and Atkinson et al. [5].
 Delayed eruptionBrown [2].
 TaurodontismBaran et al. [4] and Atkinson et al. [5].
Periodontal findings
 Gingival inflammation with oedemaBrown [2] and Baran et al. [4].
 Alveolar bone lossAbdel-Karim et al. [1], Brown [2], Davidovich et al. [3], Baran et al. [4], and Atkinson et al. [5].
 PeriodontitisDavidovich et al. [3] and Atkinson et al. [5].
 Thin enamel gingival recessionAtkinson et al. [5].
 Smooth atrophic tongue mucosaAbdel-Karim et al. [1], Brown [2], Atkinson et al. [5], and Dokal [13].
 LeukoplakiaAbdel-Karim et al. [1], Brown [2], Davidovich et al. [3], Baran et al. [4], Atkinson et al. [5], Zinsser [7], Ogden et al. [10], and Davidson and Connor [18].
 Dry mouthBaran et al. [4].
 Angular cheilitisBaran et al. [4].