| | Reference (first author) | Age | Sex | Systemic involvement | Therapy | Outcome |
| | Lopez-Estebaranz, 1993 [4] | 18 y | M | Liver dysfunction | SS, ATB, MTX, and PUVA | Cure | | Fink-Puches, 1994 [5] | 16 y | M | (—) | SS, ATB, and MTX | Cure | | Romaní, 1998 [6] | 12 y | F | (—) | ATB, MTX, and PUVA | Cure | | Ito, 2003 [7] | 12 y | M | Anemia, abdominal pain, and lymphadenopathy | SS, MTX | Cure | | Tsianakas, 2005 [8] | 9 y | M | (—) | SS, ATB, and MTX | Cure | | Herron, 2005 [9] | 8 y | F | Sepsis, DIG, ARDS, and gastrointestinal hemorrhage | SS, MTX, ATB, and cyclosporine | Cure | | Pyrpasopoulou, 2007 [10] | 17 y | F | Sepsis, anemia, and diarrhea | SS, ATB, IVIG, acyclovir, and MTX | Cure | | Helbling, 2009 [11] | 17 y | M | Lymphadenopathy | ATB, MTX | | | Zhang, 2010 [12] | 12 y | M | Pulmonary involvement | SS, ATB, and MTX | Cure | | Kaufman, 2012 [13] | 21 m | F | Laryngeal edema | SS, MTX | Cure | | Kaufman, 2012 [13] | 22 m | F | (—) | SS, ATB, acyclovir, and MTX | | | Perrin, 2012 [14] | 34 m | M | (—) | SS, ATB, acyclovir, dapsone, IVIG, and MTX | Cure | | Lin, 2012 [15] | 11 y | M | Fever, arthritis, fatigue | SS, MTX | Cure | | Rosman, 2013 [16] | 11 y | M | Central nervous system vasculitis | SS, ATB, MTX, and cyclophosphamide | Cure | | Our patient | 11 y | M | Liver dysfunction | SS, ATB, and MTX | Cure |
|
|
