A Case of Von Hippel–Lindau Disease with Bilateral Pheochromocytoma and Ectopic Hypersecretion of Intact Parathyroid Hormone in an Adolescent Girl

Table 1

Biological parameters before and after surgery.

	Before surgery	After surgery	Reference ranges
Fasting glucose level (mmol/l)	16.39	4.78	4.12–5.55
Glycated hemoglobin (%)	10.12	5.91	≤5.6
Total cholesterol (mmol/l)	11.83	5.23	3.1–5.18
Triglycerides (mmol/l)	2.43	1.21	0.57–1.71
Natremia (mmol/l)	135	140	135–145
Kalemia (mmol/l)	3.3	4	3.6–5
Creatinine (mg/L)	6	6	4–13
Calcium (mg/L)	111.2	98	88–105
Phosphate (mg/L)	44	36	27–45
Albumin (g/l)	47.22	—	35–52
Intact PTH (μg/L)	182	54	11–62
TSH (mUI/L)	0.625	—	0.12–3.4
FT4 (ng/dl)	1.31	—	0.71–1.85
Calcitonin (ng/L)	2.70	—	<10.00
24 h-urine NMN (μg/24)	3150	570	30–600
24 h-urine MN (μg/24)	40.2	12	20–345
24 h-urine sodium (mmol/24 h)	88.5	—
24 h-urine potassium (mmol/24 h)	60	—
24 h-urine calcium (mg/24 h)	200	—
24 h-proteinuria (g/24)	0.3	—	<0.3

PTH: parathormone, TSH: thyroid stimulating hormone, FT4: free-T4, NMN: normetanephrines, MN: metanephrines. The intact PTH dosage was made using 3^rd generation chemiluminescence immunoassay.