Hereditary Neuropathy with Liability to Pressure Palsies Masked by Previous Gunshots and Tuberculosis
Table 1
Nerve conduction studies at age of 35 y and 36 y in the presented patient.
Nerve
Age (y)
DL (ms)
CV (m/s)
Ampl (mV)
CD
Motor
Left median (elbow–wrist)
36
5.85
54.1
13.8
No
Left median (axilla–elbow)
36
na
52.6
15.9
No
Right median (elbow–wrist)
36
7.12
44.2
14.1
No
Left ulnar (elbow–wrist)
36
4.34
43.9
8.2
No
Left ulnar (below/above elbow)
36
na
15.0
1.86
Yes
Right ulnar (elbow–wrist)
36
4.9
52.4
10.2
No
Right ulnar (dist./prox. elbow)
36
na
19.3
9.4
No
Left ulnar (elbow–wrist)
36
4.0
32.7
6.3
No
Right ulnar (elbow–wrist)
36
4.2
36.8
6.1
No
Left peroneal (caput fibulae–ankle)
36
10.0
37.3
2.7
No
Left peroneal (dist./prox. caput fibulae)
36
na
17.5
0.24
Yes
Right peroneal (caput fibulae–ankle)
36
9.92
38.8
4.0
No
Right peroneal (dist./prox. caput fibulae)
36
na
22.9
3.4
No
Left peroneal (caput fibulae–ankle)
35
11.4
37.0
2.13
No
Right peroneal (caput fibulae–ankle)
35
9.6
43.0
7.07
No
Left peroneal (dist./prox. caput fibulae)
35
na
34.0
na
No
Right peroneal (dist./prox. caput fibulae)
35
na
23.0
na
No
Left tibial (knee–ankle)
36
4.82
44.3
11.4
No
Right tibial (knee–ankle)
36
4.71
40.9
8.5
No
Right tibial (knee–ankle)
36
4.71
40.9
8.5
No
Left tibial (knee–ankle)
35
4.4
58.0
6.67
No
Right tibial (knee–ankle)
35
5.0
47.0
8.13
No
Sensory
Left median
36
na
31.8
10.5
No
Right median
36
na
24.6
2.8
No
Right radial
36
No
28.4
7.9
No
Left sural
36
No
28.3
10.5
No
Left sural (not recordable)
35
na
na
na
na
DL: distal latency, CV: conduction velocity, Ampl: amplitude, CB: conduction block, na: not available. Amplitude difference was 79%. Amplitude difference was 91%. Amplitude higher at proximal compared to distal stimulation most likely due to nonsupramaximal stimulation distally.
