Case Report

HbS-Sicilian (δβ)0-Thalassemia: A Rare Variant of Sickle Cell

Table 1

HPLC and CBC results in patient.

6 days6 months12 months

HPLC values
HbA000
HbF89.846.241.2
HbA202.93.3
HbS10.250.955

CBC values
Hemoglobin (g/dl)1614.115.4
MCV (fL)92.367.167.5
ARC (×103/ml)n/a0.090.1