Case Report

Runaway Train: A Leaky Radiosensitive SCID with Skin Lesions and Multiple Lymphomas

Table 1

Hematologic and immunologic characteristics.

Before transplantDay 30Day 150

Blood counts
 Hemoglobin (g/dL)12,17,910,0
 Thrombocytes (×109/L)2403982
 Leukocytes (×109/L)3,93,214,1
 Lymphocytes (×109/L)0,80,56,7
 CD4 (×106/L)177
 CD8 (×106/L)277
 CD19 (×106/L)<5
Immunoglobulins
 IgG (g/L)6,12,8
 IgM (g/L)0,1<0,1
 IgA (g/L)0,4<0,1
Chimerism99%

Pretransplant data from first presentation at Oslo University Hospital. Chimerism data at day 100.