Hyper IgG4-Related Disease Presenting with Orbital Tumor and Immune Deficiency

Table 1

Laboratory values at presentation, several months into treatment while on corticosteroids and mycophenolate mofetil, and during relapse.

	IgG total (nl 694–1618 mg/dl)	IgG4 (nl 4–86 mg/dl)	IgM (nl >48 mg/dl)	ESR (nl <20 mm/hr)	CRP (nl <8 mg/dl)	Pneumococcal antibodies (nl >8/14)	Haemophilus antibodies (nl >1)	Platelets (nl 150–450)	Eosinophils (nl 15–500)
Presentation	1905	412	44	19	0.25	2/14	0.26	258	17
During treatment	1760	377	43	11	1.09	3/14	0.34	240	432
Relapse	3570	1594	20	104	9.3	4/14	0.17	250	1096