Primary Vulval Rhabdoid Tumor in an Adult: A Case Report, Immunohistochemical Profile and Literature Review

Table 1

Characteristics of the previously reported cases of EMRT of the vulva [1–10].

Author, year	Age at diagnosis (years)	Site	Primary treatment	Reported survival (months)
	19	R LMJ		38 (alive)
Perrone et al., 1989^§ [1]	30	R LMJ	Surgery	8 (dead)
	31	L vulva		138 (dead)
Matias et al., 1990 [2]	49	L LMJ	Surgery + chemotherapy	9 (dead)
Lupi et al., 1996 [3]	39	L LMJ	Surgery + chemotherapy + radiation	4 (dead)
Igarashi et al., 1998 [4]	39	L LMJ	Surgery + chemotherapy	8 (alive)
Sert et al., 1999 [5]	44	R LMJ	Surgery + chemotherapy + radiation	8 (dead)
Brand and Covert 2001 [6]	40	Mons pubis	Surgery + chemotherapy + radiation	61 (alive)
Haidopoulos et al., 2002^¥ [7]	—	Clitoris	—	—
Tzilinis et al., 2002 [8]	63	L LMJ	Surgery + radiation	30 (alive)
Argenta et al., 2007^€ [9]	35	R vulva	Surgery + radiation	40 (alive)
Narendra et al., 2010 [10]	50	R LMJ and mons pubis	Surgery + radiation	30 (alive)
Current case	25	Mons Pubis, extending to L inguinal area	Surgery	Lost followup

R: right. L: left. ^§3 cases were reported. ^¥No full text is available in PubMed. ^€The diagnosis given was EMRT/proximal epithelioid sarcoma.