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Case Reports in Medicine
Volume 2013 (2013), Article ID 692980, 3 pages
http://dx.doi.org/10.1155/2013/692980
Case Report

Sclerosing Cholangitis in Behçet’s Disease

1Department of Gastroenterology, Sahloul Hospital, 4000 Sousse, Tunisia
2Department of Radiology, Sahloul, Sousse, Tunisia

Received 14 May 2013; Revised 13 August 2013; Accepted 11 September 2013

Academic Editor: Gianfranco D. Alpini

Copyright © 2013 Aida Ben Slama Trabelsi et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Introduction. Sclerosing cholangitis is characterized by an inflammatory and fibrotic lesion of intra- and/or extrahepatic bile ducts. When a causal mechanism of a bile duct lesion is identified, the sclerosing cholangitis is considered secondary. The vasculitis, including the Behçet disease, is cited as a probable cause of the ischemia and the sclerosing cholangitis. No cases of extrahepatic secondary sclerosing cholangitis have been reported to date. Case Report. We report the first case of secondary sclerosing cholangitis of the extrahepatic bile ducts associated with Behçet disease in a male who is aged 43, with a previous history of the angio-Behçet followed by complications of thrombophlebitis and a cerebral thrombophlebitis, and who has a cholestatic jaundice. The diagnosis has been carried out by the MR cholangiopancreatography which has objectified a moderate distension of the intrahepatic bile ducts upstream of regular stacked parietal thickening of the main bile duct. The patient has been treated successfully with the ursodeoxycholic acid and the placement of a plastic stent. Conclusion. This diagnosis should be mentioned to any patient with vasculitis and who has a cholestatic jaundice.