Hyperammonemia: What Urea-lly Need to Know: Case Report of Severe Noncirrhotic Hyperammonemic Encephalopathy and Review of the Literature

Table 1

Results of serum amino acid testing.

Amino acid	Result; (nmol/mL)	Reference range; (nmol/mL)
Phosphoserine	0	<18
Phosphoethanolamine	<2	<12
Taurine	24 (L)	42–156
Asparagine	40	37–92
Serine	47 (L)	63–187
Hydroxyproline	2 (L)	4–29
Glycine	93 (L)	126–490
Glutamine	892	371–957
Aspartic acid	2	<7
Ethanolamine	<7	<67
Histidine	61	39–123
Threonine	43 (L)	85–231
Citrulline	22	17–46
Sarcosine	1	<5
Beta-alanine	13	<29
Alanine	88 (L)	200–579
Glutamic acid	43	13–113
1-Methylhistidine	0	<28
3-Methylhistidine	3	2–9
Argininosuccinic acid	0	<2
Carnosine	0	<1
Anserine	0	<1
Homocitrulline	1	<2
Arginine	28 (L)	32–120
Alpha-aminoadipic acid	2	<3
Gamma-amino-n-butyric acid	0	<2
Beta-aminoisobutyric acid	1	<5
Alpha-amino-n-butyric acid	77 (H)	9–37
Hydroxylysine	0	<2
Proline	81 (L)	97–368
Ornithine	13 (L)	38–130
Cystathionine	<1	<5
Cystine	36	3–95
Lysine	283 (H)	103–255
Methionine	41	4–44
Valine	179	136–309
Tyrosine	40	31–90
Isoleucine	54	36–107
Leucine	93	68–183
Phenylalanine	48	35–80
Tryptophan	35	29–77
Allo-isoleucine	0	<5