| Case | Author | Presenting symptoms | Age/sex | Size | Imaging | Location | Treatment | Followup/outcome |
| 1 | Friis and Hjortrup (1982) [1] | Pain, weight gain | 22F | 11 kg | IVU | PPS | RN | 36 MO/asymptomatic | 2 | Randazzo et al. (1987) [15] | Pain, bleeding | 64F | 6 cm3 | IVU, CT | Right PNS | RSR | 2 MO/asymptomatic | 3 | Ditonno et al. (1992) [16] | Pain, bleeding | 37M | 5 cm | IVU, CT, A | Right PNS | RN | N/A* | 4 | Peh et al. (1994) [17] | Weight loss/abdominal mass | 32F | 3.7 kg (7980 cm3) | US, CT | Left PNS | RN | 8 MO/asymptomatic | 5 | Angulo et al. (1994) [18] | Abdominal pain, flank pain | 53F | 336 cm3 | US, CT, A | Left PNS | RN | N/A* | 6 |
Gupta and Guleria (2011) [19] | Abdominal pain | 42M | 220 cm3 | US, CT | Right AS | RSR | N/A* | 7 | Liwnicz et al. (1994) [20] | Abdominal pain | 39F | 1.1 kg (216 cm3) | CT | Right PNS | RN | 18 MO/asymptomatic | 8 | Law et al. (1994) [21] | Incidental finding | 59F | 22.5 cm3 | CT, MRI | Left PNS | RN | N/A* | 9 | Law et al. (1994) [21] | Pain | 56F | 11 cm | IVU, CT, US, FNA | Left PNS | RN | 8 MO/asymptomatic | 10 | Mogi et al. (1998) [22] | Abdominal pain + fullness | 41F | 648 cm3 | CT, MRI | Right PNS/PHS | RSR | N/A* | 11 | Murphy et al. (2000) [23] | Abdominal pain, bleeding | 51F | ND | CT, A | Left PNS | AE | 12 MO/asymptomatic | 12 | Tsutsumi et al. (2001) [2] | Fatigue, abdominal pain | 60F | 3.5 kg (4840 cm3) | CT, A | Right PNS | RN | 60 MO/asymptomatic | 13 | Tseng et al. (2004) [24] | Abdominal fullness | 35F | 2.8 kg (3726 cm3) | US, CT, A | Right PNS | RSR | N/A* | 14 | Obara et al. (2005) [25] | Macroscopic hematuria | 31M | ND | CT, A | Right PNS | RN | N/A* | 15 | Gupta et al. (2007) [26] | Abdominal pain | 80F | 16 cm | CT, MRI | Left PNS | RN | 1 year/distal metastases | 16 |
Our Case (2011) | Asymptomatic | 39F | 1.7 kg (2898 cm3) | US, CT | Left PNS | RN | 16 MO/asymptomatic |
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