Case Report

Retroperitoneal Extrarenal Angiomyolipomas: An Evidence-Based Approach to a Rare Clinical Entity

Table 2

Detailed information on all published retroperitoneal extrarenal angiomyolipomas (1982–2011).

CaseAuthorPresenting symptomsAge/sexSizeImagingLocationTreatmentFollowup/outcome

1Friis and Hjortrup (1982) [1]Pain, weight gain22F11 kgIVUPPSRN36 MO/asymptomatic
2Randazzo et al. (1987) [15]Pain, bleeding64F6 cm3IVU, CTRight PNSRSR2 MO/asymptomatic
3Ditonno et al. (1992) [16]Pain, bleeding37M5 cmIVU, CT, ARight PNSRNN/A*
4Peh et al. (1994) [17]Weight loss/abdominal mass32F3.7 kg (7980 cm3)US, CTLeft PNSRN8 MO/asymptomatic
5Angulo et al. (1994) [18]Abdominal pain, flank pain53F336 cm3US, CT, ALeft PNSRNN/A*
6 Gupta and Guleria (2011) [19]Abdominal pain42M220 cm3US, CTRight ASRSRN/A*
7Liwnicz et al. (1994) [20]Abdominal pain39F1.1 kg (216 cm3)CTRight PNSRN18 MO/asymptomatic
8Law et al. (1994) [21]Incidental finding59F22.5 cm3CT, MRILeft PNSRNN/A*
9Law et al. (1994) [21]Pain56F11 cmIVU, CT, US, FNALeft PNSRN8 MO/asymptomatic
10Mogi et al. (1998) [22]Abdominal pain + fullness41F648 cm3CT, MRIRight PNS/PHSRSRN/A*
11Murphy et al. (2000) [23]Abdominal pain, bleeding51FNDCT, ALeft PNSAE12 MO/asymptomatic
12Tsutsumi et al. (2001) [2]Fatigue, abdominal pain60F3.5 kg (4840 cm3)CT, ARight PNSRN60 MO/asymptomatic
13Tseng et al. (2004) [24]Abdominal fullness35F2.8 kg (3726 cm3)US, CT, ARight PNSRSRN/A*
14Obara et al. (2005) [25]Macroscopic hematuria31MNDCT, ARight PNSRNN/A*
15Gupta et al. (2007) [26]Abdominal pain80F16 cmCT, MRILeft PNSRN1 year/distal metastases
16 Our Case (2011)Asymptomatic39F1.7 kg (2898 cm3)US, CTLeft PNSRN16 MO/asymptomatic

ND: not documented; A: angiography; CT: computerized tomography; MRI: magnetic resonance imaging; US: ultrasound; IVU: intravenous urography; FNA: fine needle aspiration; PNS: perinephric space; PHS: perihepatic space; PPS: peripancreatic space; AS: adrenal space; RN: radical nephrectomy; RSR: renal sparing resection; AE: angio embolization; MO: months; N/A*: follow-up information not available.