TY - JOUR A2 - Fee, Dominic B. AU - Anuradha, S. AU - Fanai, Vanlalmalsawmdawngliana PY - 2016 DA - 2016/12/21 TI - Hirayama Disease: A Rare Disease with Unusual Features SP - 5839761 VL - 2016 AB - Hirayama disease, also known as monomelic amyotrophy (MMA), is a rare cervical myelopathy that manifests itself as a self-limited, asymmetrical, slowly progressive atrophic weakness of the forearms and hands predominantly in young males. The forward displacement of the posterior dura of the lower cervical dural canal during neck flexion has been postulated to lead to lower cervical cord atrophy with asymmetric flattening. We report a case of Hirayama disease in a 25-year-old Indian man presenting with gradually progressive asymmetrical weakness and wasting of both hands and forearms along with unusual features of autonomic dysfunction and upper motor neuron lesion. SN - 2090-6668 UR - https://doi.org/10.1155/2016/5839761 DO - 10.1155/2016/5839761 JF - Case Reports in Neurological Medicine PB - Hindawi Publishing Corporation KW - ER -