Multiple Spontaneous Intracranial-Extracranial Arterial Dissections in a Patient with Osteogenesis Imperfecta

Figure 1

DWI showing (a) left acute anterior cerebral artery infarction and subacute posterior cerebral artery infarction in coronal FLAIR and (b) in postcontrast axial T1A (c); V4 segments of the vertebral arteries with a symmetrical appearance (d). Luminal narrowing along the left V2 in contrast-enhanced cervical MRA (e); hyperintensity in left V2 suggestive of intraluminal or intramural thrombus in fat-suppressed T1A (f); dissection presenting with narrowing and dilatation at the proximal part of the left A2 at 3D-TOF MRA (g) and volume rendering CTA (h). CTA was considered to be suggestive of dissected left V2, and the hyperintensity in T1A images was explained on the basis of intramural thrombus formation.

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