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Case Reports in Obstetrics and Gynecology
Volume 2014, Article ID 376231, 4 pages
Case Report

Endometriosis in a Patient with Mayer-Rokitansky-Küster-Hauser Syndrome

Ribeirão Preto School of Medicine, University of São Paulo, Avenida Bandeirantes, 3900 Ribeirão Preto, SP, Brazil

Received 7 October 2014; Accepted 12 December 2014; Published 30 December 2014

Academic Editor: Maria Grazia Porpora

Copyright © 2014 Júlia Kefalás Troncon et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


Objective. To report a case of Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) in which there were two nonfunctional rudimentary uteruses with the presence of ovarian endometrioma, corroborating that there are valid alternative theories to the existence of endometriosis, rather than Sampson’s theory alone, such as the coelomic metaplasia theory. Design. A case report. Setting. A tertiary referral center, which is also a university hospital. Patient. A fifteen-year-old patient with MRKH syndrome and endometriosis. Intervention. Laparoscopic approach for diagnostic confirmation and treatment of the endometrioma. Results. Evidence of endometriosis in a patient with no functional uterus. Conclusions. This case report and a few others that are available in the literature reinforce the possibility that coelomic metaplasia could be the origin of endometriosis. Patients with müllerian agenesis and pelvic pain should be carefully evaluated, and the presence of pelvic endometriosis should not be excluded.