Case Report

Malignant Peripheral Nerve Sheath Tumors in Children with Neurofibromatosis Type 1

Table 1

Characteristics, treatment, and outcome of patients.

CaseAge*GenderSymptoms/signsNF-1LocationSize**TreatmentOutcome

1st13FemalePain, massYesSpinal cord8 7 5
(MRI)1
Wide excision of the tumor and RTDeath
2nd13FemalePain, massYesButtockā€‰
(MRI)2
Wide excision of the tumor and RT-CTDeath
3rd9MalePain, massYesTrunkHuge
(CT scan)3
Wide excision of the tumor and RT-CTDeath
4th12FemalePain, massYesFoot (MRI)4Wide excision of the tumor and
RT-CT
Death

years, cm, 1: Figure 1, 2: Figure 2, 3: Figure 3, 4: Figure 4, RT: radiotherapy, CT: chemotherapy.