Multimodal Imaging Analysis in a Case with Congenital Fovea-Involving Retinal Macrovessel and Excellent Visual Acuity

Figure 2

Swept-source OCT angiography (a, b, c, and d) with corresponding segmentation B scan (e, f, g, and h) and en face OCT imaging (i, j, k, and l) of the right eye of a 12-year-old patient with congenital retinal macrovessel (a, e, and i). At the level of the superficial capillary plexus the principal stem of the macrovessel and two main bifurcations are noted (+). Microvascular interconnections obliterate the foveal avascular zone (a). Corresponding SS-en face OCT does not indicate any leakage from the macrovessels (b, f, and j). At the level of the deep capillary plexus there are multiple branches emanating from the principal stem and the bifurcations directed at the level of the outer plexiform layer. The latter extend and bifurcate further horizontally prior to fusing with the capillaries of the deep vascular plexus. The remaining foveal avascular zone is also depicted (arrow), considerably reduced in extent. En face OCT also clearly demonstrates the aberrant vasculature and no evidence of leakage at this level. Scans at the level of outer retina (c, g, and k) and choriocapillaris (d, h, and l) demonstrate projection artefacts of major vessels without evidence of coexisting pathology.

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