Macular Changes in a Mucopolysaccharidosis Type I Patient with Earlier Systemic Therapies

Figure 4

ERG findings. Absence of DA 0.01 ERG response and a DA 10.0 with a diminished a-wave and b-wave. LA 3.0 ERG with a diminished b-wave and absence of LA flicker 30 Hz ERG response. ERG: electroretinography; DA: dark-adapted; LA: light-adapted.