Peripapillary Pachychoroid Syndrome (PPS): Diagnosing and Treating a Rare Entity

Figure 3

OCT images of RE (a) and LE (b) with CME in the papillomacular area of both eyes and SRF in the LE. FA pictures of RE (c and d) and LE (e and f) showing several small window defects causing hyperfluorescence. Ten days later, the EDI-OCT performed (g and h) showed increased choroidal thickness and pachyvessels (asterisk, (h)) in both eyes () with additional SRF subfoveally in the RE (g); the IRF in the LE was slightly reduced, while SRF persisted (h). PFP was present temporally to the optic disc margin in the RE (white arrow, (g)). ICGA revealed pachyvessels (white arrows), especially superiorly to the ONH in the RE (i and j) and adjacent to the optic disc inferiorly in the LE (k and l), corresponding to hyperfluorescent areas of choroidal hyperpermeability noted during the mid-phase.

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