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Case Reports in Otolaryngology
Volume 2014, Article ID 172162, 3 pages
Case Report

Congenital Intralabyrinthine Cholesteatoma

1Metropolitan NeuroEar Group, The Tower Building, 1101 Wootton Parkway, Suite 900, Rockville, MD 20817, USA
2Columbia University, New York City, NY, USA

Received 18 April 2014; Accepted 21 May 2014; Published 26 June 2014

Academic Editor: Hsing-Won Wang

Copyright © 2014 Sanjay Prasad et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


A patient with a congenital intralabyrinthine cholesteatoma is presented. High-resolution computerized tomographic scans and intraoperative photomicrographs display features of intralabyrinthine extension. We discuss pathogenetic theories for the development of congenital intralabyrinthine cholesteatoma. The distinction of this condition from congenital cholesteatoma with labyrinthine erosion is discussed.