Case Report

Abnormal Congenital Location of Stapes’ Superstructure: Clinical and Embryological Implications

Table 1

Classification of congenital anomalies of the middle ear. Adapted from Teunissen and Cremers [15].

ClassMain anomalySubclassification

1Congenital stapes ankylosis

2Stapes ankylosis associated with another congenital ossicular chain anomaly

3Congenital anomaly of the ossicular chain but mobile stapes footplate(A) Discontinuity in ossicular chain
(B) Epitympanic fixation

4Congenital aplasia or severe dysplasia of oval window or round window(A) Aplasia
(B) Dysplasia
 (i) Crossing facial nerve
 (ii) Persistent stapedial artery