Case Report

A Case of Adult-Onset Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis (PFAPA) Syndrome Responsive to Tonsillectomy in Japan

Table 1

Diagnostic criteria of PFAPA.

Monthly fevers—cyclic fever at any age group
Exudative tonsillitis with negative throat culture
Cervical lymphadenitis
Possibly aphthous stomatitis
Completely asymptomatic interval between episodes
Rapid response to a single dose of corticosteroids