| | Authors | Year | Age | Sex | Laterality | Congenital defects | Middle ear malformations | Facial nerve | Surgical excision vs. biopsy | Hearing augmentation repair | Postoperative findings |
| | Taylor et al. [11] | 1961 | 31 | F | L | None | Incus, stapes | Y | Biopsy | No | Hearing unchanged | | Steffen et al. [12] | 1962 | 52 | F | R | None | Incus, stapes | | Biopsy | No | Hearing unchanged | | Noguera et al. [13] | 1964 | 19 | M | L | None | Incus, stapes | | Biopsy | OCR | Hearing unchanged | | Caplinger et al. [14] | 1967 | 34 | F | L | Auricle swelling | Malleus, incus | | Excision | No | Hearing unchanged | | Bruner et al. [15] | 1970 | 6 | F | R | None | Stapes | Y | Excision | OCR | Hearing improved, transient facial palsy | | Hociota et al. | 1975 | 50 | M | L | None | Stapes | Y | Excision | No | Facial paralysis | | Peron et al. [16] | 1975 | 20 | M | Bilateral | Developmental delay, bilateral cholesteatomas | Malleus, incus, stapes | | Autopsy | No | | | Mischke et al. [17] | 1977 | 9 | F | L | Postauricular cystic mass | Malleus, incus | Y | Biopsy | No | . | | Wine et al. [18] | 1977 | 20 | M | L | None | | Y | Biopsy | No | Hearing improved | | Abadir et al. [7] | 1978 | 21 | F | L | Microtia | Incus, stapes | Y | Excision | OCR | Hearing unchanged | | Kley et al. [19] | 1979 | 46 | F | R | None | | Y | Excision | Yes | Hearing improved | | Cannon et al. [10] | 1980 | 24 | F | R | Auricle swelling | Incus, stapes | N | Excision | No | | | Quaranta et al. [9] | 1981 | 23 | M | L | Alopecia | Incus | | Excision | No | . | | Saeger et al. [20] | 1982 | 17 | M | L | None | Incus | Y | Biopsy | No | . | | Saeger et al. [20] | 1982 | 10 | F | L | None | Malleus, incus | N | Excision | Yes | . | | Moore et al. [21] | 1984 | 5 | F | L | None | Incus, stapes | | Excision | No | | | Kartush et al. [22] | 1984 | 19 | F | R | Auricle swelling | Incus | | Biopsy | No | Hearing unchanged | | Bottrill et al. [23] | 1992 | 10 | M | R | None | Incus, stapes. | N | Excision | No | Hearing improved | | Cejas-Mendez et al. [24] | 1992 | 3 | F | L | EAC malformation | . | N | Excision | No | Hearing unchanged | | Munster et al. [25] | 1994 | 16 | M | R | None | Incus, stapes | N | Biopsy | No | . | | Namdar et al. [5] | 1995 | 6 | F | L | EAC malformation | Incus, stapes | Y | Biopsy | No | Hearing unchanged | | Hinni et al. [26] | 1996 | 9 | M | L | None | Malleus, incus, stapes | N | Excision | No | . | | Anderhuber et al. [27] | 1996 | 4 | M | L | None | Incus, stapes | N | Excision | No | Hearing unchanged | | Perry et al. [28] | 1998 | 5 | M | L | Branchial cleft cyst | Incus | Y | Biopsy | No | | | Morimoto et al. [3] | 1999 | 13 | M | L | Alopecia | Incus, stapes | Y | Excision | No | | | Supiyaphun et al. [29] | 2000 | 10 | F | L | EAC malformation | Malleus, incus, stapes | Y | Excision | No | Hearing unchanged | | Ha et al. [30] | 2000 | 3 | F | R | None | None | N | Excision | No | Hearing unchanged | | Vasama et al. [8] | 2001 | . | . | R | . | Incus | Y | . | . | . | | Buckmiller et al. [6] | 2001 | 0.75 | M | R | Facial asymmetry, bilateral preauricular pits, encephalocele, Mondini-type deformities | Incus, stapes | | Excision | No | . | | Ookuchi et al. | 2003 | 1 | F | R | None | Incus, stapes | Y | Biopsy | No | | | Simoni et al. [31] | 2003 | 0.83 | F | L | Tonsillar teratoid polyp | None | N | Excision | No | Hearing unchanged | | Enoz et al. [32] | 2006 | 14 | F | L | None | Stapes | Y | Biopsy | No | | | Yazici et al. | 2006 | 32 | F | L | None | Stapes | N | Excision | No | Hearing unchanged | | Lee et al. [33] | 2006 | 0.9166 | F | R | None | Incus, stapes | N | Excision | OCR | Hearing improved | | Boleas-Aguirre et al. [34] | 2006 | 12 | M | L | . | Incus, stapes | N | . | . | . | | Nassar et al. [35] | 2007 | 32 | M | R | None | Incus, stapes | Y | Excision | OCR | Hearing improvement, transient facial nerve palsy | | Toros et al. [36] | 2010 | 7 | F | R | Situs inversus | Incus | N | Excision | OCR | Hearing improved | | Gomez et al. | 2013 | 32 | F | L | None | Normal | | Biopsy | No | Facial nerve palsy | | Amrhein et al. [37] | 2014 | 0.83 | F | R | Branchio-oto-renal syndrome. Developmental delay, bilateral preauricular pits, ear tag, dysplastic auricle | Malleus, incus, stapes | | Excision | OCR, BAHA | Hearing unchanged | | Fois et al. [38] | 2014 | 22 | F | L | None | Incus, stapes | N | Excision | OCR | Hearing improved | | Chen et al. [39] | 2015 | 6 | F | L | Preauricular pit | | Y | Biopsy | No | Hearing unchanged | | Noda et al. [40] | 2016 | 10 | F | L | Alopecia | Stapes | Y | Biopsy | OCR | Hearing improved | | Aghazadeh et al. [1] | 2016 | 41 | M | R | None | Stapes | N | Excision | No | Hearing improved | | Ziari et al. [41] | 2016 | 39 | M | L | None | Stapes | N | Excision | No | Hearing improved | | Su et al. [42] | 2019 | 8 | F | L | Pharyngeal hamartoma | Malleus, incus | N | Excision | Yes | Hearing unchanged | | Purnell et al. [43] | 2019 | 6 | M | L | Ear tag | Incus | N | Excision | OCR | | | Current case | 2019 | 14 | F | L | Dandy–Walker | Incus, stapes | N | Excision | BAHA | Hearing improved |
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F: female, M: male, R: right, L: left, Y: yes, and N: no. All unfilled boxes indicate information that was unspecified in the case reports.
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