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Case Reports in Pathology
Volume 2012 (2012), Article ID 438505, 5 pages
http://dx.doi.org/10.1155/2012/438505
Case Report

Malignant Perivascular Epithelioid Cell Tumor of the Esophagus

1Surgical Pathology and Cytopathology Unit, Department of Medicine (DIMED), University of Padua, 35121 Padua, Italy
2General Oncology Unit, Department of Surgery, Oncology and Gastroenterology (DiSCOG), University of Padua, 35121 Padua, Italy
3Surgery Unit, Department of Surgery, Oncology and Gastroenterology (DiSCOG), University of Padua, 35121 Padua, Italy

Received 12 June 2012; Accepted 17 July 2012

Academic Editors: T. Hasebe, J. S. Khurana, and P. Kornprat

Copyright © 2012 Matteo Fassan et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Malignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was presented with ingravescent dysphagia. Although PEComas arising within the gastrointestinal tract are exceptional findings, clinicians should not exclude this class of tumors in the diagnostic investigation of a bulky lesion of the esophageal wall.