Table of Contents Author Guidelines Submit a Manuscript
Case Reports in Pathology
Volume 2014, Article ID 674094, 5 pages
http://dx.doi.org/10.1155/2014/674094
Case Report

Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the Literature

1Oral Pathology Department, Faculty of Dentistry, Alexandria University, Champollion Street, Azarita, Alexandria 21526, Egypt
2Maxillofacial and Plastic Surgery Department, Faculty of Dentistry, Alexandria University, Champollion Street, Azarita, Alexandria 21526, Egypt
3Oral Pathology Department, Faculty of Dentistry, King Abdulaziz University, P.O. Box 80200, Zip Code 21589, Jeddah 22252, Saudi Arabia
4Cairo University, 12 EL-Saraya Street, Manial, Cairo 11553, Egypt

Received 6 July 2014; Accepted 17 August 2014; Published 22 September 2014

Academic Editor: Imtiaz A. Chaudhry

Copyright © 2014 Taissir Omar et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Rhabdomyoblastic differentiation in a malignant peripheral nerve sheath tumor (MPNST) is termed malignant triton tumor (MTT), a rare neoplasm that poses a diagnostic dilemma in the differential diagnosis of neck masses and portends poor prognosis. We report a sporadic case of MTT of the neck in a 23-year-old female. We present the pathological findings. Immunohistochemistry confirmed the neurogenic origin with S-100 expression and the rhabdomyoblastic differentiation with desmin and vimentin positivity. Radical surgical excision was done. After 4 years there were no signs of recurrence or distant metastasis. The clinical, microscopic, and long-term follow-up of this case are consistent with those of a low-grade malignancy.