Case Report

Primary Villoglandular Mucinous Adenocarcinoma of the Vulva

Table 1

Reported cases of enteric type tumor in female lower genital tract.

AuthorsAgeLocationHistologyImmunohistochemistryFollow-upRef.

Tiltman and Knutzen50VulvaAdenocarcinomaNot done1 year[3]
Kennedy and Majmudar54VulvaAdenocarcinomaCEA− CK+10 years [4]
63VulvaAdenocarcinomaNot done4 years
Ghamande et al.80VulvaAdenocarcinomaCEA+19 months [5]
67VulvaAdenocarcinomaCEA+17 months
Willén et al.57VulvaAdenocarcinomaCEA+, CK+26 months[6]
Rodriguez et al.69VulvaAdenocarcinomaCEA+, CK7+,
CK20+, ER−PR−
36 months[7]
Zaidi and Conner43VulvaAdenocarcinomaCEA+, CK+18 months[8]
Liu et al.49VulvaAdenocarcinomaNot done24 months[9]
Dubé et al.58VulvaAdenocarcinomaCK7+, CK20+,
CEA+
16 months[10]
Cormio et al.58
42
Vulva
Vulva
Adenocarcinoma
Adenocarcinoma
CK7+
CK20+/−
Death
39 months
[2]
Karkouche et al.31VulvaAdenomas and adenocarcinomaAdenomas; CK7−/CK20+
Adenocarcinoma;
Not done
[11]
Vitrey et al.57VulvaAdenocarcinomaCK7−CK20+
CDX2+, CA125+/−
17 months[12]
Musella et al.66VulvaTubulovillous adenomaNot doneN/A[13]
Ciano et al.72VaginaVillous adenomaNot done6 months[14]
Ulbright et al.5VaginaPapillomaNot done12 months[15]
Fox et al.35VaginaEnteric adenocarcinomaNot doneN/A [16]
59VaginaEnteric adenocarcinomaNot doneN/A
Mortensen and Nielsen43VaginaTubulovillous adenomaCEAN/A[17]
Nagar et al.45VaginaAdenocarcinomaCK+, CEA+, p53+, ER−, PR−,18 months[18]
Mudhar et al.56VaginaAdenocarcinomaCK7−, CK20+, CEA+18 months[19]
Werner et al.67
45
Vagina
Vagina
Adenocarcinoma
Adenocarcinoma
CK7−, CK20−,
CEA+
CK7+, CK20−, CEA−
14 months
23 months
[20]
Dubé et al.64VaginaAdenocarcinomaCK7+, CK20+18 months[21]
Lee et al.61VaginaTubulovillous adenomaCK7+, CK20+, p53±N/A[22]
Tjalma and Colpaert55VaginaAdenocarcinomaCK7+, CK20+,N/A[23]
van Wessel et al.68VaginaAdenocarcinomaCEA+, CK20+, CK7+25 months[24]

Ref.; reference. N/A; not available.