Hereditary Neuropathy with Liability to Pressure Palsy: A Recurrent and Bilateral Foot Drop Case Report

Table 1

Nerve conduction studies.

(a)  

Motor nerve conduction study
Nerve	CMAP amplitude (SD) mV	CV (SD) m/s	L1 (SD) ms
First episode
Tibial
Ref.	5.8 (1.9)	43.6 (5.1)	3.96 (1)
Right	Ankle-AHM 6.8; Knee-ankle 3.1	Knee-ankle 40.0	Ankle-AHM 4.5; Knee-ankle 14.5
Peroneal
Ref.	5.1 (2.3)	39.4 (5.8)	5.5 (1.2)
Right	Ankle-EDB 5.3; Ankle 3.0; Below knee 1.6	Ankle 41.1; Below knee 29.4	Ankle-EDB 11.8; Ankle 13.5; Below knee 14.5
Second episode
Tibial
Ref.	5.8 (1.9)	43.6 (5.1)	3.96 (1)
Right	Ankle-AHM 8.4; Knee-ankle 8.0	Knee-ankle 41.8	Ankle-AHM 5.2; Knee-ankle 14.3
Left	Ankle-AHM 11.8; Knee-ankle 7.7	Knee-ankle 36.9	Ankle-AHM 3.5; Knee-ankle 13.8
Peroneal
Ref.	5.1 (2.3)	39.4 (5.8)	5.5 (1.2)
Right	Ankle-EDB 3.8; Ankle 4.3; Below knee 4.0	Ankle 43.1; Below knee 33.3	Ankle-EDB 6.0; Ankle 12.5; Below knee 14.0
Left	Ankle-EDB 5.1; Ankle 4.0; Below knee 3.6	Ankle 42.5; Below knee 36.4	Ankle-EDB 4.9; Ankle 12.2; Below knee 13.3
Median
Ref.	7 (3)	55.6 (2.9)	3.49 (0.34)
Right	Wrist-APB 5.0; Below elbow-wrist 4.9	Below elbow-wrist 41.5	Wrist-APB 4.6; Below elbow-wrist 8.7
Left	Wrist-APB 4.7; Below elbow-wrist 4.3	Below elbow-wrist 43.4	Wrist-APB 4.2; Below elbow-wrist 8.3
Ulnar
Ref.	5.5 (2)	57.8 (2.1)	6.1 (0.69)
Right	Wrist-ADM 5.2; Above elbow-below elbow 4.3; Plexus-above elbow 4.2	Below elbow-wrist 45.0; Above elbow-below elbow 32; Plexus-above elbow 42.9	Wrist-ADM 2.7; Above elbow-below elbow 9.2; Plexus-above elbow 9.9
Left	Wrist-ADM 5.8; Above elbow-below elbow 4.4; Plexus-above elbow 4.2	Below elbow-wrist 54.5; Above elbow-below elbow 41.7; Plexus-above elbow 45.8	Wrist-ADM 3.2; Above elbow-below elbow 7.7; Plexus-above elbow 8.9
Radial
Ref.	8.79 (2.3)	66.2 (7.3)	2.46 (0.72)
Right	Below elbow 10.5; Above elbow-below elbow 7.6	Below elbow 58.7	Below elbow 1.79; Above elbow-below elbow 5.2
Left	Below elbow 10.2; Above elbow-below elbow 7.8	Above elbow-below elbow 57.0	Below elbow 1.7; Above elbow-below elbow 5.1

(b)  

Sensory nerve conduction study
Nerve	Amplitude (SD) uV	L1 (SD) ms	CV (SD) m/s
First episode
Sural
Ref.	18.67 (4.39)	2.79 (0.45)	31.8 (5.6)
Right	4.7	4.3	45.2
Second episode
Sural
Ref.	18.67 (4.39)	2.79 (0.45)	31.8 (5.6)
Right	Ankle-foreleg 2.5	Ankle-foreleg 3.9	Ankle-foreleg 44.0
Left	Ankle-foreleg 2.6	Ankle-foreleg 4.0	Ankle-foreleg 44.0
Median
Ref.	38.4 (15.6)	2.84 (0.34)	65.8 (3.8)
Right	Digiti II-wrist 9.6	Digiti II-wrist 3.8	Digiti II-wrist 46.7
Left	Digiti II-wrist 25	Digiti II-wrist 4.0	Digiti II-wrist 43.8
Ulnar
Ref.	35.4 (14.7)	5.67 (0.59)	67.1 (4.7)
Right	Digiti V-wrist 13	Digiti V-wrist 3.3	Digiti V-wrist 48.0
Left	Digiti V-wrist 20	Digiti V-wrist 3.3	Digiti V-wrist 46.2
Radial
Ref.	21.4 (4.8)	2.6 (0.3)	58.1 (4.7)
Right	Interosseous digiti-forearm 22	Interosseous digiti-forearm 2.8	Interosseous digiti-forearm 44.5
Left	Interosseous digiti-forearm 20	Interosseous digiti-forearm 3.0	Interosseous digiti-forearm 42.3

CMAP: compound motor action potential; CV: conduction velocity; L1: onset latency; SD: standard deviation; AHM: abductor hallucis muscle; EDB: extensor digitorum brevis; APB: abductor pollicis brevis; ADM: abductor digiti minimi.