Hyperinsulinemic Hypoglycaemia in a Turner Syndrome with Ring (X)

Table 1

Results of the metabolites and hormones measured at the time of hypoglycemia in our child.

Hormone/metabolite	Value	Reference
Plasma glucose (mmol/L)	1.8	3.5–5.5
Serum insulin (mU/L)	7.4	<2
Serum cortisol (mmol/L)	280	<500
Serum growth hormone (mIU/L)	21	>20
Free fatty acids (mmol/L)	0.3	Raised (>0.5)
Total ketone bodies (mmol/L)	0.04 (suppressed)	Raised (>0.6)
Plasma lactate (mmol/L)	1.8	<2
Serum ammonia (µmol/L)	61	<80