Table of Contents Author Guidelines Submit a Manuscript
Case Reports in Pediatrics
Volume 2015 (2015), Article ID 691618, 5 pages
http://dx.doi.org/10.1155/2015/691618
Case Report

Congenital Portosystemic Shunt: Our Experience

1Unit of Clinical Pediatrics, Department of Medical and Pediatric Sciences, University of Catania, Via Santa Sofia, 95123 Catania, Italy
2Radiodiagnostic and Oncological Radiotherapy Unit, University Hospital “Policlinico-Vittorio Emanuele”, Via Santa Sofia, 95123 Catania, Italy

Received 7 November 2014; Revised 9 January 2015; Accepted 12 January 2015

Academic Editor: Josef Sykora

Copyright © 2015 Tiziana Timpanaro et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Linked References

  1. M. D. Stringer, “The clinical anatomy of congenital portosystemic venous shunts,” Clinical Anatomy, vol. 21, no. 2, pp. 147–157, 2008. View at Publisher · View at Google Scholar · View at Scopus
  2. N. Golewale, H. J. Paltiel, S. J. Fishman, and A. I. Alomari, “Portal vascular anomalies in Down syndrome: spectrum of clinical presentation and management approach,” Journal of Pediatric Surgery, vol. 45, no. 8, pp. 1676–1681, 2010. View at Publisher · View at Google Scholar · View at Scopus
  3. P. Writters, G. Maleaux, C. George et al., “Congenital veno-venous malformations of the liver: widely variable clinical presentations,” Journal of Gastroenterology and Hepatology, vol. 23, no. 8, part 2, pp. e390–e394, 2008. View at Google Scholar
  4. C. Sokollik, R. H. J. Bandsma, J. C. Gana, M. van den Heuvel, and S. C. Ling, “Congenital portosystemic shunt: characterization of a multisystem disease,” Journal of Pediatric Gastroenterology & Nutrition, vol. 56, no. 6, pp. 675–681, 2013. View at Publisher · View at Google Scholar · View at Scopus
  5. J. Abernethy and J. Banks, “Account of two instances of uncommon formation, in the viscera of the human body,” Philosophical Transactions of the Royal Society of London, vol. 83, pp. 59–66, 1793. View at Google Scholar
  6. G. Morgan and R. Superina, “Congenital absence of the portal vein: two cases and a proposed classification system for portasystemic vascular anomalies,” Journal of Pediatric Surgery, vol. 29, no. 9, pp. 1239–1241, 1994. View at Publisher · View at Google Scholar · View at Scopus
  7. N. H. Raskin, J. B. Price, and R. A. Fishman, “Portal-systemic encephalopathy due to congenital intrahepatic shunts,” The New England Journal of Medicine, vol. 270, pp. 225–229, 1964. View at Publisher · View at Google Scholar · View at Scopus
  8. J. H. Park, S. H. Cha, J. K. Han, and M. C. Han, “Intrahepatic portosystemic venous shunt,” American Journal of Roentgenology, vol. 155, no. 3, pp. 527–528, 1990. View at Publisher · View at Google Scholar · View at Scopus
  9. C. P. Murray, S. J. Yoo, and P. S. Babyn, “Congenital extrahepatic portosystemic shunts,” Pediatric Radiology, vol. 33, no. 9, pp. 614–620, 2003. View at Publisher · View at Google Scholar · View at Scopus
  10. M. J. Kim, J. S. Ko, J. K. Seo et al., “Clinical features of congenital portosystemic shunt in children,” European Journal of Pediatrics, vol. 171, no. 2, pp. 395–400, 2012. View at Publisher · View at Google Scholar · View at Scopus
  11. A. Watanabe, “Portal-systemic encephalopathy in non-chirrotic patients: classification of clinical types, diagnosis and treatment,” Journal of Gastroenterology and Hepatology, vol. 15, no. 9, pp. 969–979, 2000. View at Publisher · View at Google Scholar
  12. Y. Eroglu, J. Donaldson, L. G. Sorensen et al., “Improved neurocognitive function after radiologic closure of congenital portosystemic shunts,” Journal of Pediatric Gastroenterology and Nutrition, vol. 39, no. 4, pp. 410–417, 2004. View at Publisher · View at Google Scholar · View at Scopus
  13. S. Emre, R. Amon, E. Cohen, R. A. Morotti, D. Vaysman, and B. L. Shneider, “Resolution of hepatopulmonary syndrome after auxiliary partial orthotopic liver transplantation in Abernethy malformation. A case report,” Liver Transplantation, vol. 13, no. 12, pp. 1662–1668, 2007. View at Publisher · View at Google Scholar · View at Scopus
  14. J. Duprey, B. Gouin, M. F. Benazet, and J. le Gal, “Glucose intolerance and post-stimulative hypoglycaemia secondary to congenital intra-hepatic porto-caval anastomosis,” Annales de Médecine Interne, vol. 136, no. 8, pp. 655–658, 1985. View at Google Scholar · View at Scopus
  15. Y. Nishimura, G. Tajima, A. D. Bahagia et al., “Differential diagnosis of neonatal mild hypergalactosaemia detected by mass screening: clinical significance of portal vein imaging,” Journal of Inherited Metabolic Disease, vol. 27, no. 1, pp. 11–18, 2004. View at Publisher · View at Google Scholar · View at Scopus
  16. G. H. Hu, L. G. Shen, J. Yang, J. H. Mei, and Y. F. Zhu, “Insight into congenital absence of the portal vein: is it rare?” World Journal of Gastroenterology, vol. 14, no. 39, pp. 5969–5979, 2008. View at Publisher · View at Google Scholar · View at Scopus
  17. E. Alonso-Gamarra, M. Parrón, A. Pérez, C. Prieto, L. Hierro, and M. López-Santamaría, “Clinical and radiologic manifestations of congenital extrahepatic portosystemic shunts: a comprehensive review,” Radiographics, vol. 31, no. 3, pp. 707–722, 2011. View at Publisher · View at Google Scholar · View at Scopus
  18. C. Gallego, M. Miralles, C. Marín, P. Muyor, G. González, and E. García-Hidalgo, “Congenital hepatic shunts,” Radiographics, vol. 24, no. 3, pp. 755–772, 2004. View at Publisher · View at Google Scholar · View at Scopus
  19. T. Akahoshi, T. Nishizaki, K. Wakasugi et al., “Portal-systemic encephalopathy due to a congenital extrahepatic portosystemic shunt: three cases and literature review,” Hepato-Gastroenterology, vol. 47, no. 34, pp. 1113–1116, 2000. View at Google Scholar · View at Scopus
  20. T. B. Lautz, N. Tantemsapya, E. Rowell, and R. A. Superina, “Management and classification of type II congenital portosystemic shunts,” Journal of Pediatric Surgery, vol. 46, no. 2, pp. 308–314, 2011. View at Publisher · View at Google Scholar · View at Scopus
  21. Y. Matsuoka, K. Ohtomo, T. Okubo, J. Nishikawa, T. Mine, and S. Ohno, “Congenital absence of the portal vein,” Gastrointestinal Radiology, vol. 17, no. 1, pp. 31–33, 1992. View at Publisher · View at Google Scholar · View at Scopus
  22. S. Franchi-Abella, S. Branchereau, V. Lambert et al., “Complications of congenital portosystemic shunts in children: therapeutic options and outcomes,” Journal of Pediatric Gastroenterology and Nutrition, vol. 51, no. 3, pp. 322–330, 2010. View at Publisher · View at Google Scholar · View at Scopus
  23. E. S. Woodle, J. R. Thistlethwaite, J. C. Emond et al., “Successful hepatic transplantation in congenital absence of recipient portal vein,” Surgery, vol. 107, no. 4, pp. 475–479, 1990. View at Google Scholar · View at Scopus