Case Report

Goldenhar Syndrome Associated with Extensive Arterial Malformations

Figure 4

(a) Axial postcontrast CTA of the chest demonstrates a right aortic arch (white arrow). The aberrant left subclavian artery is seen extending posterior to the esophagus (thin black arrow) which helps form the complete vascular ring. The pulmonary artery was enlarged in this patient (thick black arrow). (b) Axial postcontrast CTA of the chest at a slice inferior to (a) demonstrates the ascending aorta projecting to the right (white arrow) and the aberrant left subclavian artery arising from the descending aorta and traveling posterior to the esophagus (thin black arrow). The complete vascular ring causes mass effect and narrowing of the esophagus and trachea (thick black arrow). (c) 3D surface rendered reformation of the CTA of the chest viewed in the anteroposterior dimension clearly demonstrates the right aortic arch (thick white arrow). (d) Fluoroscopic image of a barium esophagram demonstrates mass effect on the posterior esophagus (thick black arrow) created by the aberrant left subclavian artery.
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