Case Report
A Patient with MSUD: Acute Management with Sodium Phenylacetate/Sodium Benzoate and Sodium Phenylbutyrate
Table 2
Nutritional treatment plan during periods of therapy.
| | After diagnosis | 19 mo of age (before attack) | Acute management 12–72 hours | Acute Management After 72 hours | NaPB 17th day (Discharging) | NaPB 3 months | NaPB 6 months | NaPB 12 months |
| Leu (mg/day) | 336 | 360 | 0 | 360 | 360 | 390 | 420 | 450 | Isoleu (mg/day) | 161 | 298 | 300 | 290 | 290 | 342 | 390 | 410 | Valine (mg/day) | 158 | 287 | 300 | 280 | 280 | 300 | 320 | 330 | Protein (gr/kg/day) | 2,7 | 2,5 | 2,5 | 2,9 | 2,95 | 2,8 | 2,85 | 2,92 | Energy (Kcal/day) | 110 kcal/kg/day | 1198 | 1400 | 1300 | 1450 | 1580 | 1620 | 1700 |
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