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Case Reports in Pediatrics
Volume 2017, Article ID 2969473, 3 pages
https://doi.org/10.1155/2017/2969473
Case Report

Congenital Infantile Fibrosarcoma Causing Intestinal Perforation in a Newborn

1Department of Paediatric and Adolescent Surgery, Medical University of Graz, Graz, Austria
2Institute of Pathology, Medical University of Graz, Graz, Austria
3Division of Paediatric Radiology, Medical University of Graz, Graz, Austria
4Division of Pediatric Hemato-Oncology, Medical University of Graz, Graz, Austria

Correspondence should be addressed to Margarita Kaiser; ta.zarginudem@resiak.atiragram

Received 8 April 2017; Accepted 21 May 2017; Published 12 June 2017

Academic Editor: Ozgur Cogulu

Copyright © 2017 Margarita Kaiser et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Congenital infantile fibrosarcoma (CIF) is a rare malignant mesenchymal tumor and only 14 cases have been reported with gastrointestinal manifestation. We report about a female newborn delivered per emergency cesarean section at 34 weeks of gestation. Postnatally, she rapidly developed an acute abdomen and sonographic evidence of intestinal perforation requiring laparotomy on the first day of life. A perforated 2 × 3 cm sized spherical tumorous structure of the jejunum was identified. Due to unknown histopathology at this point and unclear resectional margins, she received a temporary ileostomy, which was closed two months later. Histopathology revealed a congenital intestinal fibrosarcoma without the characteristic ETV6-NTRK3 fusion transcript. In conclusion, this rare tumor must be considered as differential diagnosis of intestinal perforations in newborns.