Case Report

Hemorrhagic Shock after Neonatal Circumcision: Severe Congenital Factor XIII Deficiency

Table 3

Coagulation factor levels tested.

Lab reference rangeNewborn reference range (mean ± standard Deviation)Initial results (DOL 4)Repeat results (DOL 6)

Fibrinogen (mg/dL)163–463153297
Factor II (%)77–13858 ± 144957
Factor V (%)75–13790 ± 253186
Factor VII (%)71–14785 ± 2681
Factor VIII (%)57–15289 ± 33212202
Factor IX (%)80–14749 ± 174773
Factor X (%)76–14646 ± 144249
Factor XI (%)78–13357 ± 1663
Factor XII (%)47–17344 ± 1746
Factor XIII (%)69–14389 ± 2420

Source: reference [1].