Case Report
Hemorrhagic Shock after Neonatal Circumcision: Severe Congenital Factor XIII Deficiency
Table 3
Coagulation factor levels tested.
| | Lab reference range | Newborn reference range (mean ± standard Deviation) | Initial results (DOL 4) | Repeat results (DOL 6) |
| Fibrinogen (mg/dL) | 163–463 | — | 153 | 297 | Factor II (%) | 77–138 | 58 ± 14 | 49 | 57 | Factor V (%) | 75–137 | 90 ± 25 | 31 | 86 | Factor VII (%) | 71–147 | 85 ± 26 | 81 | | Factor VIII (%) | 57–152 | 89 ± 33 | 212 | 202 | Factor IX (%) | 80–147 | 49 ± 17 | 47 | 73 | Factor X (%) | 76–146 | 46 ± 14 | 42 | 49 | Factor XI (%) | 78–133 | 57 ± 16 | — | 63 | Factor XII (%) | 47–173 | 44 ± 17 | — | 46 | Factor XIII (%) | 69–143 | 89 ± 24 | — | 20 |
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