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Case Reports in Radiology
Volume 2014, Article ID 283902, 5 pages
Case Report

Ewing Sarcoma of the Kidney: A Rare Entity

1Diagnostic Radiology Resident, A. C. Camargo Hospital, Sao Paulo, SP, Brazil
2Department of Diagnostic Radiology, The University of Texas M. D. Anderson Cancer Center, 1515 Holcombe Boulevard, Houston, TX 77030, USA

Received 26 November 2013; Accepted 19 December 2013; Published 9 January 2014

Academic Editors: C. Chaskis, E. Z. Kapsalaki, and C. Preul

Copyright © 2014 Maria Fernanda Arruda Almeida et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


Ewing sarcoma and primitive peripheral neuroectodermal tumor (PNET) are high-grade malignant tumors typically found in children and adolescents. These tumors belong to the family of small round cell tumors and are of neuroectodermal origin. Primary Ewing sarcoma of the kidney is rare and because of that is an infrequent differential diagnosis in urologic malignancies. Renal PNET mostly presents with nonspecific symptoms such as hematuria and abdominal pain. The imaging findings are uncharacteristic. The diagnosis is based on the histology, immunohistochemistry, and molecular pathologic findings. Once PNET has been diagnosed, multimodal treatment is indicated. Despite all treatment options, the prognosis of those with metastatic disease is poor.