TY - JOUR A2 - Littlejohn, G. O. A2 - Soy, M. A2 - Orellana, C. AU - Bonilla-Abadía, Fabio AU - Pérez, Manuel A. AU - Muñoz-Buitrón, Evelyn AU - Rosales, Joaquín D. AU - Cañas, Carlos A. AU - Tobón, Gabriel J. PY - 2013 DA - 2013/04/23 TI - Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome SP - 831708 VL - 2013 AB - Primary Sjögren's syndrome (pSS) is an autoimmune disorder of the exocrine glands presenting with progressive ocular and oral dryness, parotid gland enlargement, and often with extraglandular manifestations. In this group of patients the risk of development of non-Hodgkin's lymphoma is 16-fold compared to healthy population, mainly of the MALT lymphoma type. This case reports a 52-year-old woman with pSS developing a progressively growing mass at face and neck compatible with blastoid variant mantle cell lymphoma and a fatal outcome. SN - 2090-6889 UR - https://doi.org/10.1155/2013/831708 DO - 10.1155/2013/831708 JF - Case Reports in Rheumatology PB - Hindawi Publishing Corporation KW - ER -